Teratomas are the tumor derived from the three germ cell layers. Teratomas presented in the middle ear and eustachian tube are extremely rare. Eustachian tube teratoma extends either up to the middle ear, external ear, and mastoid or down to the nasopharynx. Tumors extending up to the middle ear usually present with recurrent ear drainage and rarely present with facial palsy. Our patient underwent transoral removal of pedunculated nasopharyngeal mass prior to excision of the ear canal mass. This lesion could be suspected as a "dumb-bell" teratoma involving the nasopharynx, eustachian tube, the middle ear and the external ear canal. This case demonstrates the importance of ear examination when managing nasopharyngeal lesions that originate from the eustachian tube and middle ear, even if the patient is an infant. We report a case of eustachian mature teratoma in a female child.