A case of head and neck rhabdomyosarcoma with pancreatic metastasis

Abstract

Rhabdomyosarcoma is a malignant tumor of mesenchymal origin. It is relatively common in childhood but relatively rare in adults. Common primary sites are the head and neck, extremities, and genitourinary tract. Lung, bone, lymph node, and bone marrow are common metastasis sites. Histologically, it can be classified into embryonal, botryoid, alveolar, and pleomorphic rhabdomyosarcoma. The alveolar subtype accounts for approximately 20%, and its prognosis is poor. The management of rhabdomyosarcoma usually involves a combination of surgery, radiotherapy, and chemotherapy. Metastatic pancreas rhabdomyosarcoma is rare. We experienced a case of alveolar-type maxillary rhabdomyosarcoma that metastasized to the pancreas, and we report this with a review of the literature.

저자들은 안면부 동통 주소로 내원한 46세 여환에게서 상악동에서 발견된 횡문근육종을 부분 상악동 절개 및 림프절 제거 후 동시 화학/방사선요법 시행하였으나 췌장에 전이된 예를 1예 경험하였기에 문헌고찰과 함께 보고하는 바이다.